Primary Lymphedema

Written by Diane Sievert
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Primary lymphedema is a condition that results from unknown causes or other vascular anomalies like lymphangioma, hemangioma, Klippel Trenaury and Port Wine Stain. Unlike secondary lymphedema, primary lymphedema is not acquired in any way. And unfortunately, there's no way to pinpoint who's at risk.

A Guide to Primary Lymphedema

Primary lymphedema can arise at one of three times: birth, the onset of puberty (praecox) or adulthood (tarda). More often than not, the symptoms of primary lymphedema come on rather slowly and can go on for quite some time before they are recognized. Primary lymphedema can also affect different parts of the body: one individual may only get swelling in the right arm while another individual could experience swelling in all four limbs and the trunk.

Unfortunately, those individuals who have lymphedema-all-over are often misdiagnosed as overweight. In these cases, however, diets simply do not work; if an individual is strictly adhering to a diet and not losing any weight, primary lymphedema could be to blame. In addition to undergoing the usual lymphedema treatments (manual lymph drainage and compression therapies), those suffering from lymphedema-all-over should also consider taking Benzo-pyrones as this medication has proven most effective.

Another thing to consider is that primary lymphedema can also affect the gut and lungs. If the gut is targeted, it can result in protein-losing enteropathy and intestinal lymphangiectasia. Also be aware that just because the lymphedema symptoms were first noticed in the arm doesn't mean the other limbs and areas of the body aren't at risk.

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